Juvenile ossifying fibroma is a rare fibro-osseous neoplasm seen in the pediatric age group of 5 to 15 years. It has been recognized as a separate histopathologic entity among the fibro-osseous group of lesions. Occasionally, it may grow aggressively and extend to involve the orbits and skull base, resulting in serious cosmetic and functional problems. We present a case of a juvenile ossifying fibroma arising below the skull base of a 9-year-old boy. This case demonstrates that cemento-ossifying fibroma in case of maxilla grow to considerable size before causing symptoms because of the remodeling of the surrounding bony compartment and intraoral sublabial approach can be used to excise lesion completely even at the skull base.